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KMID : 0367419890320070995
Journal of Korean Pediatric Society
1989 Volume.32 No. 7 p.995 ~ p.1000
A Case of Cytophagic Histiocytic Panniculitis
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Abstract
Cytophagic histiocytic panniculitis is a chronic, benign, visceral and cutaneous histiocytic (cyto- phagic) paniculitis, progressing to liver dysfunction, jaundice and a terminal hemorrhagic diathesis. We have experienced a case of cytophagic histiocytic panniculitis in an 11 year old male who had developed recurrent fever and subcutaneous nooules since infancy, progressing to liver dysfunction, jaundice and hemorrhagic diathesis. The noaular biopsy also showed a characteristic histiocytic panniculitis, such as bean bag cell. A brief review of literatures was made.
KEYWORD
Cytophagic histiocytic panniculitis, Terminal bleeding diathesis, Bean bag cell
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